Olliers disease: features of the hands

Description

A 14-year-old boy attended our services for orthopaedic evaluation due to the development of multiple enchondromatous lesions. Clinical examination of the hands revealed painless swollen digits of asymmetric lengths (figure 1). Plain film radiographs demonstrated extensive bilateral expansile lytic lesions of metacarpals and phalanges with diffuse matrix calcification resulting in cortical thinning, which is in keeping with Ollier's disease (figure 2). With no features concerning for malignancy in the hands, this patient is being followed up annually and remained symptom free at his last review.

Figure 1

Topographical view of a patient's hands with Ollier's disease.

Figure 2

Plain radiography; anteroposterior of left and right hands depicting multiple radiolucent expansile lesions with cortical thinning of the metacarpal and phalanges.

Ollier's disease is defined as multiple enchondromas with asymmetric distribution that are...

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